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Reduced Right Ventricular Native Myocardial T(1) in Anderson-Fabry Disease: Comparison to Pulmonary Hypertension and Healthy Controls

AIMS: Anderson-Fabry disease (AFD) is characterized by progressive multiorgan accumulation of intracellular sphingolipids due to α-galactosidase A enzyme deficiency, resulting in progressive ventricular hypertrophy, heart failure, arrhythmias, and death. Decreased native (non-contrast) left ventricu...

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Detalles Bibliográficos
Autores principales:	Pagano, Joseph J., Chow, Kelvin, Khan, Aneal, Michelakis, Evangelos, Paterson, Ian, Oudit, Gavin Y., Thompson, Richard B.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Public Library of Science 2016
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4909219/ https://www.ncbi.nlm.nih.gov/pubmed/27305064 http://dx.doi.org/10.1371/journal.pone.0157565

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