Quantification of Diaphragm Mechanics in Pompe Disease Using Dynamic 3D MRI

BACKGROUND: Diaphragm weakness is the main reason for respiratory dysfunction in patients with Pompe disease, a progressive metabolic myopathy affecting respiratory and limb-girdle muscles. Since respiratory failure is the major cause of death among adult patients, early identification of respirator...

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Detalles Bibliográficos
Autores principales: Mogalle, Katja, Perez-Rovira, Adria, Ciet, Pierluigi, Wens, Stephan C. A., van Doorn, Pieter A., Tiddens, Harm A. W. M., van der Ploeg, Ans T., de Bruijne, Marleen
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Public Library of Science 2016
Materias:
Research Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4938606/
https://www.ncbi.nlm.nih.gov/pubmed/27391236
http://dx.doi.org/10.1371/journal.pone.0158912

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4938606/
https://www.ncbi.nlm.nih.gov/pubmed/27391236
http://dx.doi.org/10.1371/journal.pone.0158912

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