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Pulmonary arterial hypertension associated with hereditary spherocytosis and splenectomy in a patient with a mutation in the BMPR2 gene

There is some question about the relationship between hereditary spherocytosis (HS) and pulmonary arterial hypertension, even associated with splenectomy. The finding of BMPR2 mutations in our patient suggests that other factors are necessary for the development of the disease, and perhaps, the inci...

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Detalles Bibliográficos
Autores principales: Baloira, Adolfo, Bastos, María, Pousada, Guillermo, Valverde, Diana
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4974420/
https://www.ncbi.nlm.nih.gov/pubmed/27525076
http://dx.doi.org/10.1002/ccr3.610