Long-term treatment of phenylketonuria with a new medical food containing large neutral amino acids

BACKGROUND/OBJECTIVES: Phenylketonuria (PKU) is an autosomal recessive disease caused by deficient activity of phenylalanine hydroxylase. A low phenylalanine (Phe) diet is used to treat PKU. The diet is very restrictive, and dietary adherence tends to decrease as patients get older. Methods to impro...

Descripción completa

Detalles Bibliográficos
Autores principales: Concolino, D, Mascaro, I, Moricca, M T, Bonapace, G, Matalon, K, Trapasso, J, Radhakrishnan, G, Ferrara, C, Matalon, R, Strisciuglio, P
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Nature Publishing Group 2017
Materias:
Original Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5222990/
https://www.ncbi.nlm.nih.gov/pubmed/27623981
http://dx.doi.org/10.1038/ejcn.2016.166

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5222990/
https://www.ncbi.nlm.nih.gov/pubmed/27623981
http://dx.doi.org/10.1038/ejcn.2016.166

Ejemplares similares