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The Imaging Findings of Erdheim–Chester Disease: A Multimodality Approach to Diagnosis and Staging

Erdheim–Chester disease (ECD) is a rare, non-Langerhans histiocytic disorder. The most common manifestations consist of polyostotic sclerotic lesions with the majority of cases also demonstrating soft tissue involvement of the sinuses, retroperitoneum, large vessels, heart, lungs, and central nervou...

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Detalles Bibliográficos
Autores principales: Martineau, Patrick, Pelletier-Galarneau, Matthieu, Zeng, Wanzhen
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2017
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5314669/
https://www.ncbi.nlm.nih.gov/pubmed/28217025
http://dx.doi.org/10.4103/1450-1147.181149