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Childhood Polyarthritis As Early Manifestation of Autoimmune Polyendocrinopathy with Candidiasis and Ectodermal Dystrophy Syndrome

Autoimmune polyendocrinopathy with candidiasis and ectodermal dystrophy (APECED) is a rare disorder of immune dysregulation caused by mutations in the autoimmune regulator (AIRE) gene. Individuals affected with APECED develop a clinical syndrome characterized by ectodermal abnormalities, autoantibod...

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Detalles Bibliográficos
Autores principales: Gutierrez, Maria J., Gilson, Julieta, Zacharias, Jamie, Ishmael, Faoud, Bingham, C. April
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2017
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5394715/
https://www.ncbi.nlm.nih.gov/pubmed/28458664
http://dx.doi.org/10.3389/fimmu.2017.00377