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in vivo localization of the neuronal ceroid lipofuscinosis proteins, CLN3 and CLN7, at endogenous expression levels

The neuronal ceroid lipofuscinoses are a group of recessively inherited, childhood-onset neurodegenerative conditions. Several forms are caused by mutations in genes encoding putative lysosomal membrane proteins. Studies of the cell biology underpinning these disorders are hampered by the poor antig...

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Detalles Bibliográficos
Autores principales:	Mohammed, Alamin, O'Hare, Megan B., Warley, Alice, Tear, Guy, Tuxworth, Richard I.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Academic Press 2017
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5441185/ https://www.ncbi.nlm.nih.gov/pubmed/28365214 http://dx.doi.org/10.1016/j.nbd.2017.03.015

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