Cargando…

Variables influencing fluorimetric N-sulfoglucosamine sulfohydrolase (SGSH) activity measurement in brain homogenates

Deficient N-sulfoglucosamine sulfohydrolase (SGSH) enzyme activity causes mucopolysaccharidosis (MPS) type IIIA. A fluorimetric SGSH activity assay is commonly used to examine patient cells. Here, we modified this method for brain homogenates and define the parameters for assay linearity. SGSH activ...

Descripción completa

Detalles Bibliográficos
Autores principales:	Whyte, Lauren S., Hopwood, John J., Hemsley, Kim M., Lau, Adeline A.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Elsevier 2015
Materias:	Short Communication
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5475436/ https://www.ncbi.nlm.nih.gov/pubmed/28652977 http://dx.doi.org/10.1016/j.ymgmr.2015.10.005

Ejemplares similares

Intracerebroventricular dosing of N-sulfoglucosamine sulfohydrolase in mucopolysaccharidosis IIIA mice reduces markers of brain lysosomal dysfunction
por: Magat, Jenna, et al.
Publicado: (2022)

AAVrh10 Vector Corrects Disease Pathology in MPS IIIA Mice and Achieves Widespread Distribution of SGSH in Large Animal Brains
por: Hocquemiller, Michaël, et al.
Publicado: (2019)

A novel mutation in SGSH causing Sanfillipo type 3A Mucopolysaccharidoses in an Indian family
por: Singh, Jyotsna, et al.
Publicado: (2018)

Fluorimetric Quantification of Brimonidine Tartrate in Eye Drops
por: Sunitha, G., et al.
Publicado: (2013)

A novel mutation of SGSH and clinical features analysis of mucopolysaccharidosis type IIIA
por: Li, Xiaohua, et al.
Publicado: (2018)

An Engineered sgsh Mutant Zebrafish Recapitulates Molecular and Behavioural Pathobiology of Sanfilippo Syndrome A/MPS IIIA
por: Douek, Alon M., et al.
Publicado: (2021)

Fluorimetric Immunoassay for Multianalysis of Aflatoxins
por: Kanungo, Lizy, et al.
Publicado: (2013)

Lysosomal gene Hexb displays haploinsufficiency in a knock-in mouse model of Alzheimer’s disease
por: Whyte, Lauren S., et al.
Publicado: (2022)

Determination of 5-S-cysteinyldopa in melanomas with a fluorimetric method.
por: Rorsman, H., et al.
Publicado: (1973)

A Fluorimetric Sensor for Detection of One Living Cell
por: Vitecek, Jan, et al.
Publicado: (2007)

Comparison of Spectrophotometric and Fluorimetric Methods in Evaluation of Biotinidase Deficiency
por: Işeri-Erten, Sevgin Özlem, et al.
Publicado: (2016)

Nanomaterials-Based Fluorimetric Methods for MicroRNAs Detection
por: La, Ming, et al.
Publicado: (2015)

Dual Sensitivity—Potentiometric and Fluorimetric—Ion-Selective Membranes
por: Stelmach, Emilia, et al.
Publicado: (2021)

Functional correction of neurological and somatic disorders at later stages of disease in MPS IIIA mice by systemic scAAV9-hSGSH gene delivery
por: Fu, Haiyan, et al.
Publicado: (2016)

A microfluidic device with fluorimetric detection for intracellular components analysis
por: Kwapiszewski, Radosław, et al.
Publicado: (2011)

New Spectrophotometric and Fluorimetric Methods for Determination of Fluoxetine in Pharmaceutical Formulations
por: Darwish, Ibrahim A., et al.
Publicado: (2009)

Miniaturized Fluorimetric Method for Quantification of Zinc in Dry Dog Food
por: Martins, Rute C., et al.
Publicado: (2020)

Fluorimetric Analysis of Five Amino Acids in Chocolate: Development and Validation
por: Synaridou, Maria S., et al.
Publicado: (2021)

Comparison of oil-in-water emulsions prepared by ultrasound, high-pressure homogenization and high-speed homogenization
por: Zhou, Lei, et al.
Publicado: (2021)

Protein-templated copper nanoclusters for fluorimetric determination of human serum albumin
por: Lettieri, Mariagrazia, et al.
Publicado: (2021)

Development of miniaturized fluorimetric device for caffeine determination using a smartphone
por: Luchiari, Natália da Costa, et al.
Publicado: (2019)

Hybrid Sol–Gel Matrices Doped with Colorimetric/Fluorimetric Imidazole Derivatives †
por: Sousa, Rui P. C. L., et al.
Publicado: (2021)

The Role of N and S Doping on Photoluminescent Characteristics of Carbon Dots from Palm Bunches for Fluorimetric Sensing of Fe(3+) Ion
por: Saengsrichan, Aphinan, et al.
Publicado: (2022)

Nucleobase–Guanidiniocarbonyl-Pyrrole Conjugates as Novel Fluorimetric Sensors for Single Stranded RNA
por: Ban, Željka, et al.
Publicado: (2017)

A Zinpyr-1-based Fluorimetric Microassay for Free Zinc in Human Serum
por: Alker, Wiebke, et al.
Publicado: (2019)

Fluorimetric Method for the Determination of Histidine in Random Human Urine Based on Zone Fluidics
por: Alevridis, Antonios, et al.
Publicado: (2020)

Highly sensitive naphthalimide based Schiff base for the fluorimetric detection of Fe(3+)
por: Jothi, Dhanapal, et al.
Publicado: (2021)

A highly sensitive fluorimetric protocol based on isoindole formation for determination of gabapentin
por: Attia, Tamer Z., et al.
Publicado: (2019)

Inter-individual variability contrasts with regional homogeneity in the human brain DNA methylome
por: Illingworth, Robert S., et al.
Publicado: (2015)

New fluorimetric assay of horseradish peroxidase using sesamol as substrate and its application to EIA
por: Arakawa, Hidetoshi, et al.
Publicado: (2012)

Development of Functional Phthalocyanine-Based Associate towards an Effective Fluorimetric Detection of Hg(II)
por: Du, Guang-Xin, et al.
Publicado: (2018)

Fluorimetric detection of reserpine in mouse serum through online post-column electrochemical derivatization
por: Chen, Ning, et al.
Publicado: (2018)

A novel fluorimetric method for determination of pseudoephedrine hydrochloride in pharmaceutical formulations and blood serum
por: FARAJZADEH, Nazli, et al.
Publicado: (2020)

Determination of berberine hydrochloride using a fluorimetric method with silica nanoparticles as a probe
por: Liu, Qing, et al.
Publicado: (2018)

Fluorescent molecularly imprinted polymer nanocomposite for solid-phase extraction and fluorimetric determination of hydrochlorothiazide
por: Abo Dena, Ahmed S., et al.
Publicado: (2023)

The Influence of Paracetamol on the Penetration of Sorafenib and Sorafenib N-Oxide Through the Blood–Brain Barrier in Rats
por: Karbownik, Agnieszka, et al.
Publicado: (2020)

Appraisal of fluorimetric assay of aryl hydrocarbon (benzo(alpha)pyrene) hydroxylase in cultured human lymphocytes.
por: Trieff, N. M., et al.
Publicado: (1978)

Haemoglobin interference and increased sensitivity of fluorimetric assays for quantification of low-parasitaemia Plasmodium infected erythrocytes
por: Moneriz, Carlos, et al.
Publicado: (2009)

A Modified Fluorimetric Method for Determination of Hydrogen Peroxide Using Homovanillic Acid Oxidation Principle
por: Paital, Biswaranjan
Publicado: (2014)

Formation and Fluorimetric Characterization of Micelles in a Micro-flow Through System with Static Micro Mixer
por: Schuch, Michael, et al.
Publicado: (2007)

Cannot write session to /tmp/vufind_sessions/sess_dvtu0vu1semmag8i0odaf87tm7