Evaluation of mitochondrial bioenergetics, dynamics, endoplasmic reticulum-mitochondria crosstalk, and reactive oxygen species in fibroblasts from patients with complex I deficiency

Mitochondrial complex I (CI) deficiency is the most frequent cause of oxidative phosphorylation (OXPHOS) disorders in humans. In order to benchmark the effects of CI deficiency on mitochondrial bioenergetics and dynamics, respiratory chain (RC) and endoplasmic reticulum (ER)-mitochondria communicati...

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Detalles Bibliográficos
Autores principales: Leipnitz, Guilhian, Mohsen, Al-Walid, Karunanidhi, Anuradha, Seminotti, Bianca, Roginskaya, Vera Y., Markantone, Desiree M., Grings, Mateus, Mihalik, Stephanie J., Wipf, Peter, Van Houten, Bennett, Vockley, Jerry
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Nature Publishing Group UK 2018
Materias:
Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5773529/
https://www.ncbi.nlm.nih.gov/pubmed/29348607
http://dx.doi.org/10.1038/s41598-018-19543-3

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5773529/
https://www.ncbi.nlm.nih.gov/pubmed/29348607
http://dx.doi.org/10.1038/s41598-018-19543-3

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