Clinical management and outcomes of patients with Hermansky-Pudlak syndrome pulmonary fibrosis evaluated for lung transplantation

Pulmonary fibrosis is a progressive, fatal manifestation of Hermansky-Pudlak syndrome (HPS). Some patients with advanced HPS pulmonary fibrosis undergo lung transplantation despite their disease-associated bleeding tendency; others die while awaiting donor organs. The objective of this study is to d...

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Detalles Bibliográficos
Autores principales: El-Chemaly, Souheil, O’Brien, Kevin J., Nathan, Steven D., Weinhouse, Gerald L., Goldberg, Hilary J., Connors, Jean M., Cui, Ye, Astor, Todd L., Camp, Philip C., Rosas, Ivan O., Lemma, Merte, Speransky, Vladislav, Merideth, Melissa A., Gahl, William A., Gochuico, Bernadette R.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Public Library of Science 2018
Materias:
Research Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5856338/
https://www.ncbi.nlm.nih.gov/pubmed/29547626
http://dx.doi.org/10.1371/journal.pone.0194193

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5856338/
https://www.ncbi.nlm.nih.gov/pubmed/29547626
http://dx.doi.org/10.1371/journal.pone.0194193

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