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Endothelial dysfunction in pulmonary arterial hypertension: loss of cilia length regulation upon cytokine stimulation

Pulmonary arterial hypertension (PAH) is a syndrome characterized by progressive lung vascular remodelling, endothelial cell (EC) dysfunction, and excessive inflammation. The primary cilium is a sensory antenna that integrates signalling and fine tunes EC responses to various stimuli. Yet, cilia fun...

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Detalles Bibliográficos
Autores principales: Dummer, Anneloes, Rol, Nina, Szulcek, Robert, Kurakula, Kondababu, Pan, Xiaoke, Visser, Benjamin I., Bogaard, Harm Jan, DeRuiter, Marco C., Goumans, Marie-José, Hierck, Beerend P.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: SAGE Publications 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5858634/
https://www.ncbi.nlm.nih.gov/pubmed/29480152
http://dx.doi.org/10.1177/2045894018764629