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Super-resolution imaging reveals the sub-diffraction phenotype of Zellweger Syndrome ghosts and wild-type peroxisomes
Peroxisomes are ubiquitous cell organelles involved in many metabolic and signaling functions. Their assembly requires peroxins, encoded by PEX genes. Mutations in PEX genes are the cause of Zellweger Syndrome spectrum (ZSS), a heterogeneous group of peroxisomal biogenesis disorders (PBD). The size...
Autores principales: | Soliman, Kareem, Göttfert, Fabian, Rosewich, Hendrik, Thoms, Sven, Gärtner, Jutta |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Nature Publishing Group UK
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5958128/ https://www.ncbi.nlm.nih.gov/pubmed/29773809 http://dx.doi.org/10.1038/s41598-018-24119-2 |
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