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Radiological pleuroparenchymal fibroelastosis associated to limited cutaneous systemic sclerosis: a case report
BACKGROUND: Pleuroparenchymal fibroelastosis (PPFE) is a very rare interstitial lung disease (ILD) characterized by progressive fibrotic lesions of the visceral pleura and the sub-pleural parenchyma, affecting predominantly the upper lobes. PPFE may occur in different contextes like bone marrow or l...
Autores principales: | , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5960118/ https://www.ncbi.nlm.nih.gov/pubmed/29776440 http://dx.doi.org/10.1186/s12890-018-0641-5 |