Cargando…

Radiological pleuroparenchymal fibroelastosis associated to limited cutaneous systemic sclerosis: a case report

BACKGROUND: Pleuroparenchymal fibroelastosis (PPFE) is a very rare interstitial lung disease (ILD) characterized by progressive fibrotic lesions of the visceral pleura and the sub-pleural parenchyma, affecting predominantly the upper lobes. PPFE may occur in different contextes like bone marrow or l...

Descripción completa

Detalles Bibliográficos
Autores principales: Hassoun, D., Dirou, S., Arrigoni, P. P., Durant, C., Hamidou, M., Néel, A., Agard, C.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5960118/
https://www.ncbi.nlm.nih.gov/pubmed/29776440
http://dx.doi.org/10.1186/s12890-018-0641-5