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Lamins and bone disorders: current understanding and perspectives

Lamin A/C is a major constituent of the nuclear lamina implicated in a number of genetic diseases, collectively known as laminopathies. The most severe forms of laminopathies feature, among other symptoms, congenital scoliosis, osteoporosis, osteolysis or delayed cranial ossification. Importantly, s...

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Detalles Bibliográficos
Autores principales: Gargiuli, Chiara, Schena, Elisa, Mattioli, Elisabetta, Columbaro, Marta, D'Apice, Maria Rosaria, Novelli, Giuseppe, Greggi, Tiziana, Lattanzi, Giovanna
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Impact Journals LLC 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5978267/
https://www.ncbi.nlm.nih.gov/pubmed/29854317
http://dx.doi.org/10.18632/oncotarget.25071