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Angiotensin, transforming growth factor β and aortic dilatation in Marfan syndrome: Of mice and humans()
Marfan syndrome is consequent upon mutations in FBN1, which encodes the extracellular matrix microfibrillar protein fibrillin-1. The phenotype is characterised by development of thoracic aortic aneurysm. Current understanding of the pathogenesis of aneurysms in Marfan syndrome focuses upon abnormal...
| Autores principales: | , |
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| Formato: | Online Artículo Texto |
| Lenguaje: | English |
| Publicado: |
Elsevier
2018
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| Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5988480/ https://www.ncbi.nlm.nih.gov/pubmed/29876507 http://dx.doi.org/10.1016/j.ijcha.2018.02.009 |