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Metabolic Changes Associated With Muscle Expression of SOD1(G93A)

Amyotrophic lateral sclerosis (ALS) is a severe neurodegenerative disorder, classified into sporadic or familial forms and characterized by motor neurons death, muscle atrophy, weakness, and paralysis. Among the familial cases of ALS, approximately 20% are caused by dominant mutations in the gene co...

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Detalles Bibliográficos
Autores principales: Dobrowolny, Gabriella, Lepore, Elisa, Martini, Martina, Barberi, Laura, Nunn, Abigail, Scicchitano, Bianca Maria, Musarò, Antonio
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6048270/
https://www.ncbi.nlm.nih.gov/pubmed/30042688
http://dx.doi.org/10.3389/fphys.2018.00831