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Sirolimus in Infants with Multiple Cardiac Rhabdomyomas Associated with Tuberous Sclerosis Complex
INTRODUCTION: Cardiac rhabdomyomas represent a frequent manifestation of tuberous sclerosis. Tumor growth, mainly prenatally, can result in intrauterine fetal or neonatal deaths in almost 10% of patients. CASE REPORT: We treated 3 consecutive infants aged less than 12 months with sirolimus, an oral...
Autores principales: | Lucchesi, Maurizio, Chiappa, Enrico, Giordano, Flavio, Mari, Francesco, Genitori, Lorenzo, Sardi, Iacopo |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
S. Karger AG
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6062714/ https://www.ncbi.nlm.nih.gov/pubmed/30057537 http://dx.doi.org/10.1159/000490662 |
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