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Why, when and how to investigate primary ciliary dyskinesia in adult patients with bronchiectasis

Bronchiectasis represents the final pathway of several infectious, genetic, immunologic or allergic disorders. Accurate and prompt identification of the underlying cause is a key recommendation of several international guidelines, in order to tailor treatment appropriately. Primary ciliary dyskinesi...

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Detalles Bibliográficos
Autores principales: Contarini, Martina, Shoemark, Amelia, Rademacher, Jessica, Finch, Simon, Gramegna, Andrea, Gaffuri, Michele, Roncoroni, Luca, Seia, Manuela, Ringshausen, Felix C., Welte, Tobias, Blasi, Francesco, Aliberti, Stefano, Chalmers, James D.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6101078/
https://www.ncbi.nlm.nih.gov/pubmed/30151188
http://dx.doi.org/10.1186/s40248-018-0143-6