Cargando…
Hemophagocytic Lymphohistiocytosis Complicating Systemic Sarcoidosis
Hemophagocytic lymphohistiocytosis (HLH) is a rare, life-threatening hyperinflammatory syndrome characterized by histiocyte proliferation and hemophagocytosis. Primary HLH is caused by genetic defects, whereas secondary HLH occurs in the setting of underlying diseases, such as infections, malignanci...
Autores principales: | , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Cureus
2018
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6101461/ https://www.ncbi.nlm.nih.gov/pubmed/30131931 http://dx.doi.org/10.7759/cureus.2838 |