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Hemophagocytic Lymphohistiocytosis Complicating Systemic Sarcoidosis

Hemophagocytic lymphohistiocytosis (HLH) is a rare, life-threatening hyperinflammatory syndrome characterized by histiocyte proliferation and hemophagocytosis. Primary HLH is caused by genetic defects, whereas secondary HLH occurs in the setting of underlying diseases, such as infections, malignanci...

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Detalles Bibliográficos
Autores principales: Abughanimeh, Omar, Qasrawi, Ayman, Abu Ghanimeh, Mouhanna
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6101461/
https://www.ncbi.nlm.nih.gov/pubmed/30131931
http://dx.doi.org/10.7759/cureus.2838