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Immune‐Mediated Myocarditis in Fabry Disease Cardiomyopathy

BACKGROUND: Glycosphingolipid accumulation in Fabry cells generates a proinflammatory response that may influence disease evolution and responsiveness to enzyme replacement therapy. This study evaluated incidence, mechanism, and impact of myocarditis in Fabry disease cardiomyopathy (FDCM). METHODS A...

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Detalles Bibliográficos
Autores principales: Frustaci, Andrea, Verardo, Romina, Grande, Claudia, Galea, Nicola, Piselli, Pierluca, Carbone, Iacopo, Alfarano, Maria, Russo, Matteo Antonio, Chimenti, Cristina
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6201436/
https://www.ncbi.nlm.nih.gov/pubmed/30371172
http://dx.doi.org/10.1161/JAHA.118.009052