Cargando…
Immune‐Mediated Myocarditis in Fabry Disease Cardiomyopathy
BACKGROUND: Glycosphingolipid accumulation in Fabry cells generates a proinflammatory response that may influence disease evolution and responsiveness to enzyme replacement therapy. This study evaluated incidence, mechanism, and impact of myocarditis in Fabry disease cardiomyopathy (FDCM). METHODS A...
Autores principales: | Frustaci, Andrea, Verardo, Romina, Grande, Claudia, Galea, Nicola, Piselli, Pierluca, Carbone, Iacopo, Alfarano, Maria, Russo, Matteo Antonio, Chimenti, Cristina |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
John Wiley and Sons Inc.
2018
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6201436/ https://www.ncbi.nlm.nih.gov/pubmed/30371172 http://dx.doi.org/10.1161/JAHA.118.009052 |
Ejemplares similares
-
Pemphigus‐associated cardiomyopathy: report of autoimmune myocarditis and review of literature
por: Frustaci, Andrea, et al.
Publicado: (2021) -
Removal of cardiac AL amyloid with positive remodelling of cardiomyocytes and of restrictive cardiomyopathy
por: Frustaci, Andrea, et al.
Publicado: (2022) -
Inflammation of Conduction Tissue in Patients with Arrhythmic Phenotype of Myocarditis
por: Frustaci, Andrea, et al.
Publicado: (2020) -
Hypertrophy of unaffected cardiomyocytes correlates with severity of cardiomyopathy in female patients with Fabry disease
por: Chimenti, Cristina, et al.
Publicado: (2021) -
Downregulation of Mannose-6-Phosphate Receptors in Fabry Disease Cardiomyopathy: A Potential Target for Enzyme Therapy Enhancement
por: Frustaci, Andrea, et al.
Publicado: (2022)