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Effects of metformin on congenital muscular dystrophy type 1A disease progression in mice: a gender impact study

Congenital muscular dystrophy with laminin α2 chain-deficiency (LAMA2-CMD) is a severe muscle disorder with complex underlying pathogenesis. We have previously employed profiling techniques to elucidate molecular patterns and demonstrated significant metabolic impairment in skeletal muscle from LAMA...

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Detalles Bibliográficos
Autores principales:	Fontes-Oliveira, Cibely C., M. Soares Oliveira, Bernardo, Körner, Zandra, M. Harandi, Vahid, Durbeej, Madeleine
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Nature Publishing Group UK 2018
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6214987/ https://www.ncbi.nlm.nih.gov/pubmed/30389963 http://dx.doi.org/10.1038/s41598-018-34362-2

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