FKBP8 Enhances Protein Stability of the CLC-1 Chloride Channel at the Plasma Membrane

Mutations in the skeletal muscle-specific CLC-1 chloride channel are associated with the human hereditary disease myotonia congenita. The molecular pathophysiology underlying some of the disease-causing mutations can be ascribed to defective human CLC-1 protein biosynthesis. CLC-1 protein folding is...

Descripción completa

Detalles Bibliográficos
Autores principales: Peng, Yi-Jheng, Lee, Yi-Ching, Fu, Ssu-Ju, Chien, Yun-Chia, Liao, Yi-Fan, Chen, Tsung-Yu, Jeng, Chung-Jiuan, Tang, Chih-Yung
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2018
Materias:
Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6320802/
https://www.ncbi.nlm.nih.gov/pubmed/30487393
http://dx.doi.org/10.3390/ijms19123783

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6320802/
https://www.ncbi.nlm.nih.gov/pubmed/30487393
http://dx.doi.org/10.3390/ijms19123783

Ejemplares similares