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FKBP8 Enhances Protein Stability of the CLC-1 Chloride Channel at the Plasma Membrane

Mutations in the skeletal muscle-specific CLC-1 chloride channel are associated with the human hereditary disease myotonia congenita. The molecular pathophysiology underlying some of the disease-causing mutations can be ascribed to defective human CLC-1 protein biosynthesis. CLC-1 protein folding is...

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Detalles Bibliográficos
Autores principales:	Peng, Yi-Jheng, Lee, Yi-Ching, Fu, Ssu-Ju, Chien, Yun-Chia, Liao, Yi-Fan, Chen, Tsung-Yu, Jeng, Chung-Jiuan, Tang, Chih-Yung
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2018
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6320802/ https://www.ncbi.nlm.nih.gov/pubmed/30487393 http://dx.doi.org/10.3390/ijms19123783

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