Peripheral Primitive Neuroectodermal Tumor of the Ovary: The Report of Two Rare Cases
Peripheral primitive neuroectodermal tumor (pPNET) is a highly aggressive small round cell tumor belonging to PNET/Ewing sarcoma family. Ovarian tumors composed of primitive neuroectodermal elements are extremely rare. Herein we reported two cases of peripheral primitive neuroectodermal tumors of ov...
Autores principales: | , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
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Iranian Society of Pathology
2018
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6358556/ https://www.ncbi.nlm.nih.gov/pubmed/30774687 |
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author | Nili, Fatemeh Sedighi Moghadam Pour, Azadeh Moradi Tabriz, Hedieh Sedighi Moghadam Pour, Parisa Saffar, Hana |
author_facet | Nili, Fatemeh Sedighi Moghadam Pour, Azadeh Moradi Tabriz, Hedieh Sedighi Moghadam Pour, Parisa Saffar, Hana |
author_sort | Nili, Fatemeh |
collection | PubMed |
description | Peripheral primitive neuroectodermal tumor (pPNET) is a highly aggressive small round cell tumor belonging to PNET/Ewing sarcoma family. Ovarian tumors composed of primitive neuroectodermal elements are extremely rare. Herein we reported two cases of peripheral primitive neuroectodermal tumors of ovary in two patients with different clinical presentations. Definite diagnoses were made based on the histomorphology and immunohistochemistry results. With respect to different clinical behaviors, treatment modalities and prognosis of peripheral primitive neuroectodermal tumors compared to other known ovarian neoplasms, it is essential to consider this entity as a differential diagnosis in ovarian tumors especially in young patients. |
format | Online Article Text |
id | pubmed-6358556 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2018 |
publisher | Iranian Society of Pathology |
record_format | MEDLINE/PubMed |
spelling | pubmed-63585562019-02-15 Peripheral Primitive Neuroectodermal Tumor of the Ovary: The Report of Two Rare Cases Nili, Fatemeh Sedighi Moghadam Pour, Azadeh Moradi Tabriz, Hedieh Sedighi Moghadam Pour, Parisa Saffar, Hana Iran J Pathol Case Report Peripheral primitive neuroectodermal tumor (pPNET) is a highly aggressive small round cell tumor belonging to PNET/Ewing sarcoma family. Ovarian tumors composed of primitive neuroectodermal elements are extremely rare. Herein we reported two cases of peripheral primitive neuroectodermal tumors of ovary in two patients with different clinical presentations. Definite diagnoses were made based on the histomorphology and immunohistochemistry results. With respect to different clinical behaviors, treatment modalities and prognosis of peripheral primitive neuroectodermal tumors compared to other known ovarian neoplasms, it is essential to consider this entity as a differential diagnosis in ovarian tumors especially in young patients. Iranian Society of Pathology 2018 2018-09-25 /pmc/articles/PMC6358556/ /pubmed/30774687 Text en © 2018, IRANIAN JOURNAL OF PATHOLOGY This is an open-access article distributed under the terms of the Creative Commons Attribution-noncommercial 4.0 International License, (https://creativecommons.org/licenses/by-nc/4.0/) which permits copy and redistribute the material just in noncommercial usages, provided the original work is properly cited. |
spellingShingle | Case Report Nili, Fatemeh Sedighi Moghadam Pour, Azadeh Moradi Tabriz, Hedieh Sedighi Moghadam Pour, Parisa Saffar, Hana Peripheral Primitive Neuroectodermal Tumor of the Ovary: The Report of Two Rare Cases |
title | Peripheral Primitive Neuroectodermal Tumor of the Ovary: The Report of Two Rare Cases |
title_full | Peripheral Primitive Neuroectodermal Tumor of the Ovary: The Report of Two Rare Cases |
title_fullStr | Peripheral Primitive Neuroectodermal Tumor of the Ovary: The Report of Two Rare Cases |
title_full_unstemmed | Peripheral Primitive Neuroectodermal Tumor of the Ovary: The Report of Two Rare Cases |
title_short | Peripheral Primitive Neuroectodermal Tumor of the Ovary: The Report of Two Rare Cases |
title_sort | peripheral primitive neuroectodermal tumor of the ovary: the report of two rare cases |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6358556/ https://www.ncbi.nlm.nih.gov/pubmed/30774687 |
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