Peripheral Primitive Neuroectodermal Tumor of the Ovary: The Report of Two Rare Cases

Peripheral primitive neuroectodermal tumor (pPNET) is a highly aggressive small round cell tumor belonging to PNET/Ewing sarcoma family. Ovarian tumors composed of primitive neuroectodermal elements are extremely rare. Herein we reported two cases of peripheral primitive neuroectodermal tumors of ov...

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Autores principales: Nili, Fatemeh, Sedighi Moghadam Pour, Azadeh, Moradi Tabriz, Hedieh, Sedighi Moghadam Pour, Parisa, Saffar, Hana
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Iranian Society of Pathology 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6358556/
https://www.ncbi.nlm.nih.gov/pubmed/30774687
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author Nili, Fatemeh
Sedighi Moghadam Pour, Azadeh
Moradi Tabriz, Hedieh
Sedighi Moghadam Pour, Parisa
Saffar, Hana
author_facet Nili, Fatemeh
Sedighi Moghadam Pour, Azadeh
Moradi Tabriz, Hedieh
Sedighi Moghadam Pour, Parisa
Saffar, Hana
author_sort Nili, Fatemeh
collection PubMed
description Peripheral primitive neuroectodermal tumor (pPNET) is a highly aggressive small round cell tumor belonging to PNET/Ewing sarcoma family. Ovarian tumors composed of primitive neuroectodermal elements are extremely rare. Herein we reported two cases of peripheral primitive neuroectodermal tumors of ovary in two patients with different clinical presentations. Definite diagnoses were made based on the histomorphology and immunohistochemistry results. With respect to different clinical behaviors, treatment modalities and prognosis of peripheral primitive neuroectodermal tumors compared to other known ovarian neoplasms, it is essential to consider this entity as a differential diagnosis in ovarian tumors especially in young patients.
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spelling pubmed-63585562019-02-15 Peripheral Primitive Neuroectodermal Tumor of the Ovary: The Report of Two Rare Cases Nili, Fatemeh Sedighi Moghadam Pour, Azadeh Moradi Tabriz, Hedieh Sedighi Moghadam Pour, Parisa Saffar, Hana Iran J Pathol Case Report Peripheral primitive neuroectodermal tumor (pPNET) is a highly aggressive small round cell tumor belonging to PNET/Ewing sarcoma family. Ovarian tumors composed of primitive neuroectodermal elements are extremely rare. Herein we reported two cases of peripheral primitive neuroectodermal tumors of ovary in two patients with different clinical presentations. Definite diagnoses were made based on the histomorphology and immunohistochemistry results. With respect to different clinical behaviors, treatment modalities and prognosis of peripheral primitive neuroectodermal tumors compared to other known ovarian neoplasms, it is essential to consider this entity as a differential diagnosis in ovarian tumors especially in young patients. Iranian Society of Pathology 2018 2018-09-25 /pmc/articles/PMC6358556/ /pubmed/30774687 Text en © 2018, IRANIAN JOURNAL OF PATHOLOGY This is an open-access article distributed under the terms of the Creative Commons Attribution-noncommercial 4.0 International License, (https://creativecommons.org/licenses/by-nc/4.0/) which permits copy and redistribute the material just in noncommercial usages, provided the original work is properly cited.
spellingShingle Case Report
Nili, Fatemeh
Sedighi Moghadam Pour, Azadeh
Moradi Tabriz, Hedieh
Sedighi Moghadam Pour, Parisa
Saffar, Hana
Peripheral Primitive Neuroectodermal Tumor of the Ovary: The Report of Two Rare Cases
title Peripheral Primitive Neuroectodermal Tumor of the Ovary: The Report of Two Rare Cases
title_full Peripheral Primitive Neuroectodermal Tumor of the Ovary: The Report of Two Rare Cases
title_fullStr Peripheral Primitive Neuroectodermal Tumor of the Ovary: The Report of Two Rare Cases
title_full_unstemmed Peripheral Primitive Neuroectodermal Tumor of the Ovary: The Report of Two Rare Cases
title_short Peripheral Primitive Neuroectodermal Tumor of the Ovary: The Report of Two Rare Cases
title_sort peripheral primitive neuroectodermal tumor of the ovary: the report of two rare cases
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6358556/
https://www.ncbi.nlm.nih.gov/pubmed/30774687
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