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Mysterious quad of constrictive pericarditis, recurrent pleural effusions, bone involvement and interstitial lung disease
Erdheim–Chester disease (ECD) is a rare multisystemic non-Langerhans cell histiocytic neoplasm. The rarity of the disease and heterogenous clinical presentations often leads to delayed diagnosis. Historically, ECD lacked effective treatment and the prognosis was poor. Following the recent discovery...
Autores principales: | , , , , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Oxford University Press
2019
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6440277/ https://www.ncbi.nlm.nih.gov/pubmed/30949353 http://dx.doi.org/10.1093/omcr/omz015 |