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Metabolic disease and ABHD6 alter the circulating bis(monoacylglycerol)phosphate profile in mice and humans

Bis(monoacylglycerol)phosphate (BMP) is a phospholipid that is crucial for lipid degradation and sorting in acidic organelles. Genetic and drug-induced lysosomal storage disorders (LSDs) are associated with increased BMP concentrations in tissues and in the circulation. Data on BMP in disorders othe...

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Detalles Bibliográficos
Autores principales: Grabner, Gernot F., Fawzy, Nermeen, Pribasnig, Maria A., Trieb, Markus, Taschler, Ulrike, Holzer, Michael, Schweiger, Martina, Wolinski, Heimo, Kolb, Dagmar, Horvath, Angela, Breinbauer, Rolf, Rülicke, Thomas, Rabl, Roland, Lass, Achim, Stadlbauer, Vanessa, Hutter-Paier, Birgit, Stauber, Rudolf E., Fickert, Peter, Zechner, Rudolf, Marsche, Gunther, Eichmann, Thomas O., Zimmermann, Robert
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The American Society for Biochemistry and Molecular Biology 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6495172/
https://www.ncbi.nlm.nih.gov/pubmed/30894461
http://dx.doi.org/10.1194/jlr.M093351