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Optimising amino acid absorption: essential to improve nitrogen balance and metabolic control in phenylketonuria
It has been nearly 70 years since the discovery that strict adherence to a diet low in phenylalanine prevents severe neurological sequelae in patients with phenylalanine hydroxylase deficiency (phenylketonuria; PKU). Today, dietary treatment with restricted phenylalanine intake supplemented with non...
Autores principales: | MacDonald, Anita, Singh, Rani H., Rocha, Júlio César, van Spronsen, Francjan J. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Cambridge University Press
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6536823/ https://www.ncbi.nlm.nih.gov/pubmed/30284526 http://dx.doi.org/10.1017/S0954422418000173 |
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