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Optimising amino acid absorption: essential to improve nitrogen balance and metabolic control in phenylketonuria

It has been nearly 70 years since the discovery that strict adherence to a diet low in phenylalanine prevents severe neurological sequelae in patients with phenylalanine hydroxylase deficiency (phenylketonuria; PKU). Today, dietary treatment with restricted phenylalanine intake supplemented with non...

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Detalles Bibliográficos
Autores principales: MacDonald, Anita, Singh, Rani H., Rocha, Júlio César, van Spronsen, Francjan J.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cambridge University Press 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6536823/
https://www.ncbi.nlm.nih.gov/pubmed/30284526
http://dx.doi.org/10.1017/S0954422418000173