Cargando…

Mechanisms of thrombocytopenia in platelet-type von Willebrand disease

Platelet-type von Willebrand disease is an inherited platelet disorder characterized by thrombocytopenia with large platelets caused by gain-of-function variants in GP1BA leading to enhanced GPIbα-von Willebrand factor (vWF) interaction. GPIbα and vWF play a role in megakaryocytopoiesis, thus we aim...

Descripción completa

Detalles Bibliográficos
Autores principales:	Bury, Loredana, Malara, Alessandro, Momi, Stefania, Petito, Eleonora, Balduini, Alessandra, Gresele, Paolo
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Ferrata Storti Foundation 2019
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6601082/ https://www.ncbi.nlm.nih.gov/pubmed/30655369 http://dx.doi.org/10.3324/haematol.2018.200378

Ejemplares similares

Platelet dysfunction in platelet-type von Willebrand disease due to the constitutive triggering of the Lyn-PECAM1 inhibitory pathway
por: Bury, Loredana, et al.
Publicado: (2021)

Outside-In Signalling Generated by a Constitutively Activated Integrin α(IIb)β(3) Impairs Proplatelet Formation in Human Megakaryocytes
por: Bury, Loredana, et al.
Publicado: (2012)

Learning the Ropes of Platelet Count Regulation: Inherited Thrombocytopenias
por: Bury, Loredana, et al.
Publicado: (2021)

Diagnostic Value of Measuring Platelet Von Willebrand Factor in Von Willebrand Disease
por: Casonato, Alessandra, et al.
Publicado: (2016)

Interactions of adenoviruses with platelets and coagulation and the vaccine-induced immune thrombotic thrombocytopenia syndrome
por: Gresele, Paolo, et al.
Publicado: (2021)

Relevance of platelet desialylation and thrombocytopenia in type 2B von Willebrand disease: preclinical and clinical evidence
por: Dupont, Annabelle, et al.
Publicado: (2019)

Of von Willebrand factor and platelets
por: Bryckaert, Marijke, et al.
Publicado: (2014)

Platelets and Airway Diseases
por: Momi, Stefania, et al.
Publicado: (2017)

The impact of aberrant von Willebrand factor-GPIbα interaction on megakaryopoiesis and platelets in humanized type 2B von Willebrand disease model mouse
por: Kanaji, Sachiko, et al.
Publicado: (2022)

Von Willebrand disease type Vicenza: In search of a classification for the archetype of reduced von Willebrand factor survival
por: Casonato, Alessandra, et al.
Publicado: (2021)

A comparative study in patients with type 2 von Willebrand disease using 4 different platelet-dependent von Willebrand factor assays
por: Colpani, Paola, et al.
Publicado: (2023)

Pseudo (Platelet-type) von Willebrand disease in pregnancy: a case report
por: Grover, Neetu, et al.
Publicado: (2013)

Increased Von Willebrand factor, decreased ADAMTS13 and thrombocytopenia in melioidosis
por: Birnie, Emma, et al.
Publicado: (2017)

Terminal Platelet Production is Regulated by Von Willebrand Factor
por: Poirault-Chassac, Sonia, et al.
Publicado: (2013)

Loss of matrix metalloproteinase 2 in platelets reduces arterial thrombosis in vivo
por: Momi, Stefania, et al.
Publicado: (2009)

Desialylation of platelets induced by Von Willebrand Factor is a novel mechanism of platelet clearance in dengue
por: Riswari, Silvita Fitri, et al.
Publicado: (2019)

Hemophilia and von Willebrand disease: Factor VIII and von Willebrand factor
por: Sharma, Prashant
Publicado: (2019)

Reply to “Comment on: A comparative study in type 2 von Willebrand disease patients using four different platelet-dependent von Willebrand factor assays”
por: Colpani, Paola, et al.
Publicado: (2023)

Platelet size for distinguishing between inherited thrombocytopenias and immune thrombocytopenia: a multicentric, real life study
por: Noris, Patrizia, et al.
Publicado: (2013)

Differences in von Willebrand factor function in type 2A von Willebrand disease and left ventricular assist device‐induced acquired von Willebrand syndrome
por: Deconinck, Shannen, et al.
Publicado: (2018)

Correction: Increased Von Willebrand factor, decreased ADAMTS13 and thrombocytopenia in melioidosis
por: Birnie, Emma, et al.
Publicado: (2020)

Subcellular platelet factor VIII antigen and von Willebrand factor
Publicado: (1975)

Changes of von Willebrand Factor during Pregnancy in Women with and without von Willebrand Disease
por: Castaman, Giancarlo
Publicado: (2013)

Genetic Variation in the von Willebrand Factor Gene in Swedish von Willebrand Disease Patients
por: Manderstedt, Eric, et al.
Publicado: (2018)

Involvement of von Willebrand factor and botrocetin in the thrombocytopenia induced by Bothrops jararaca snake venom
por: Thomazini, Camila Martos, et al.
Publicado: (2021)

Von Willebrand Disease: An Overview
por: Bharati, K. Pavani, et al.
Publicado: (2011)

Hyperglycemia-Induced Platelet Activation in Type 2 Diabetes Is Resistant to Aspirin but Not to a Nitric Oxide–Donating Agent
por: Gresele, Paolo, et al.
Publicado: (2010)

A Comparative Evaluation of an Automated Functional Assay for Von Willebrand Factor Activity in Type 1 Von Willebrand Disease
por: Lai, Shiue-Wei, et al.
Publicado: (2021)

Pharmacokinetic-Pharmacodynamic Comparison of Recombinant and Plasma-Derived von Willebrand Factor in Patients with von Willebrand Disease Type 3
por: Bauer, Alexander, et al.
Publicado: (2023)

Effects of Plasmin on von Willebrand Factor and Platelets: A Narrative Review
por: van der Vorm, Lisa N., et al.
Publicado: (2018)

Platelet-independent adhesion of calcium-loaded erythrocytes to von Willebrand factor
por: Smeets, Michel W. J., et al.
Publicado: (2017)

Von Willebrand factor propeptide and pathophysiological mechanisms in European and Iranian patients with type 3 von Willebrand disease enrolled in the 3WINTERS‐IPS study
por: Pagliari, Maria Teresa, et al.
Publicado: (2022)

Letter in response to Colpani et al “A comparative study in type 2 von Willebrand disease patients using four different platelet-dependent von Willebrand factor assays”
por: Favaloro, Emmanuel J.
Publicado: (2023)

Porcine and Canine von Willebrand Factor and von Willebrand Disease: Hemostasis, Thrombosis, and Atherosclerosis Studies
por: Nichols, Timothy C., et al.
Publicado: (2010)

Classification of von Willebrand disease in the context of modern contemporary von Willebrand factor testing methodologies
por: Favaloro, Emmanuel J.
Publicado: (2020)

Improving diagnosis of von Willebrand disease: Reference ranges for von Willebrand factor multimer distribution
por: Vangenechten, Inge, et al.
Publicado: (2020)

von Willebrand factor levels in the diagnosis of von Willebrand disease: a systematic review and meta-analysis
por: Kalot, Mohamad A., et al.
Publicado: (2021)

Presence of factor VIII-related antigen in blood platelets of patients with Von Willebrand's disease
por: BOUMA, B. N., et al.
Publicado: (1975)

Platelet degranulation and bleeding phenotype in a large cohort of Von Willebrand disease patients
por: Swinkels, Maurice, et al.
Publicado: (2022)

Correction: Platelet-independent adhesion of calcium-loaded erythrocytes to von Willebrand factor
por: Smeets, Michel W. J., et al.
Publicado: (2018)

Cannot write session to /tmp/vufind_sessions/sess_v6d760nm8p8148ppi9mphkl5io