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A Case of Focal Dermal Hypoplasia (Goltze Syndrome) Masquerading as Lingual Tonsillar Hypertrophy

Focal dermal hypoplasia is a rare condition affecting organ systems of mesodermal origin. We present a rare case of this condition presenting with apparent palatine tonsillar regrowth and outline our management. Airway management should always be a consideration in this rare condition.

Detalles Bibliográficos
Autores principales: Roberts, Samuel T., Shein, Greg, Jacobson, Ian
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6604470/
https://www.ncbi.nlm.nih.gov/pubmed/31316852
http://dx.doi.org/10.1155/2019/9536256