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Evans Syndrome in Childhood: Long Term Follow-Up and the Evolution in Primary Immunodeficiency or Rheumatological Disease

Evans syndrome (ES) is a rare but challenging condition, characterized by recurrent and refractory cytopenia episodes. Recent discoveries highlighted that an appropriate diagnostic workup is fundamental to identify an underlying immune dysregulation such as primary immunodeficiencies or a rheumatolo...

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Detalles Bibliográficos
Autores principales: Rivalta, Beatrice, Zama, Daniele, Pancaldi, Giovanni, Facchini, Elena, Cantarini, Maria Elena, Miniaci, Angela, Prete, Arcangelo, Pession, Andrea
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6664023/
https://www.ncbi.nlm.nih.gov/pubmed/31396497
http://dx.doi.org/10.3389/fped.2019.00304