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Evans Syndrome in Childhood: Long Term Follow-Up and the Evolution in Primary Immunodeficiency or Rheumatological Disease
Evans syndrome (ES) is a rare but challenging condition, characterized by recurrent and refractory cytopenia episodes. Recent discoveries highlighted that an appropriate diagnostic workup is fundamental to identify an underlying immune dysregulation such as primary immunodeficiencies or a rheumatolo...
Autores principales: | Rivalta, Beatrice, Zama, Daniele, Pancaldi, Giovanni, Facchini, Elena, Cantarini, Maria Elena, Miniaci, Angela, Prete, Arcangelo, Pession, Andrea |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Frontiers Media S.A.
2019
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6664023/ https://www.ncbi.nlm.nih.gov/pubmed/31396497 http://dx.doi.org/10.3389/fped.2019.00304 |
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