Familial pulmonary fibrosis: a heterogeneous spectrum of presentations

OBJECTIVE: To describe the clinical, functional, and radiological features of index cases of familial pulmonary fibrosis (FPF) in Brazil. METHODS: We evaluated 35 patients with FPF - of whom 18 (51.4%) were women - with a median age of 66.0 years (range, 35.5-89.3 years). All of the patients complet...

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Detalles Bibliográficos
Autores principales: Hortense, Ana Beatriz, dos Santos, Marcel Koenigkam, Wada, Danilo, Fabro, Alexandre Todorovic, Lima, Mariana, Rodrigues, Silvia, Calado, Rodrigo Tocantins, Baddini-Martinez, José
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Sociedade Brasileira de Pneumologia e Tisiologia 2019
Materias:
Original Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6715161/
https://www.ncbi.nlm.nih.gov/pubmed/31188976
http://dx.doi.org/10.1590/1806-3713/e20180079

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6715161/
https://www.ncbi.nlm.nih.gov/pubmed/31188976
http://dx.doi.org/10.1590/1806-3713/e20180079

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