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Basement membrane collagens and disease mechanisms

Basement membranes (BMs) are specialised extracellular matrix (ECM) structures and collagens are a key component required for BM function. While collagen IV is the major BM collagen, collagens VI, VII, XV, XVII and XVIII are also present. Mutations in these collagens cause rare multi-systemic diseas...

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Detalles Bibliográficos
Autores principales: Gatseva, Anna, Sin, Yuan Yan, Brezzo, Gaia, Van Agtmael, Tom
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Portland Press Ltd. 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6744580/
https://www.ncbi.nlm.nih.gov/pubmed/31387942
http://dx.doi.org/10.1042/EBC20180071