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8. An autoinflammatory syndrome resembling Castleman’s disease with excellent response to IL-6 blockade

INTRODUCTION: Autoinflammatory diseases are an emerging group, characterised by recurrent inflammatory episodes due to dysregulated innate immunity. Common features include fevers, rash, arthralgia, lymphadenopathy and systemic symptoms. Castleman’s disease is a rare lymphoproliferative disease, ass...

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Detalles Bibliográficos
Autores principales: Chakravorty, Mithun, Mathew, Rengi
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Oxford University Press 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6761477/
http://dx.doi.org/10.1093/rap/rkz023.002