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Deficiency of Mitochondrial Aspartate-Glutamate Carrier 1 Leads to Oligodendrocyte Precursor Cell Proliferation Defects Both In Vitro and In Vivo

Aspartate-Glutamate Carrier 1 (AGC1) deficiency is a rare neurological disease caused by mutations in the solute carrier family 25, member 12 (SLC25A12) gene, encoding for the mitochondrial aspartate-glutamate carrier isoform 1 (AGC1), a component of the malate–aspartate NADH shuttle (MAS), expresse...

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Detalles Bibliográficos
Autores principales: Petralla, Sabrina, Peña-Altamira, Luis Emiliano, Poeta, Eleonora, Massenzio, Francesca, Virgili, Marco, Barile, Simona Nicole, Sbano, Luigi, Profilo, Emanuela, Corricelli, Mariangela, Danese, Alberto, Giorgi, Carlotta, Ostan, Rita, Capri, Miriam, Pinton, Paolo, Palmieri, Ferdinando, Lasorsa, Francesco Massimo, Monti, Barbara
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6769484/
https://www.ncbi.nlm.nih.gov/pubmed/31514314
http://dx.doi.org/10.3390/ijms20184486