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2045 The role of TGFβ in driving early cystic fibrosis lung disease

OBJECTIVES/SPECIFIC AIMS: Transforming growth factor-beta (TGFβ) is a genetic modifier of cystic fibrosis (CF) lung disease. TGFβ’s pulmonary levels in young CF patients and its mechanism of action in CF are unknown. We examined TGFβ levels in children with CF and investigated responses of human air...

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Detalles Bibliográficos
Autores principales: Kramer, Elizabeth L., Hardie, William, Hudock, Kristin, Davidson, Cynthia, Ostmann, Alicia, Clancy, John P.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cambridge University Press 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6798400/
http://dx.doi.org/10.1017/cts.2018.139