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Large neutral amino acid status in association with P:T ratio and diet in adult and pediatric patients with phenylketonuria
BACKGROUND: Intake of large neutral amino acids (LNAA) may inhibit phenylalanine (PHE) transport across the blood brain barrier and assist with blood PHE control in patients with phenylketonuria (PKU). We evaluated the interrelationship between LNAA in plasma and diet on Phe:Tyr (P:T) ratio in patie...
Autores principales: | Douglas, Teresa D., Nucci, Anita M., Berry, Ann M., Henes, Sarah T., Singh, Rani H. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
John Wiley & Sons, Inc.
2019
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6850973/ https://www.ncbi.nlm.nih.gov/pubmed/31741827 http://dx.doi.org/10.1002/jmd2.12076 |
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