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Low fat diets increase survival of a mouse model of spinal muscular atrophy

Spinal muscular atrophy (SMA) is a neuromuscular disorder leading to paralysis and death. Recent evidence shows increased susceptibility to dyslipidemia and liver steatosis in patients. Here, we provide evidence that low fat diets nearly double survival in Smn(2B/−) mice, a model for SMA, independen...

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Detalles Bibliográficos
Autores principales: Deguise, Marc‐Olivier, Chehade, Lucia, Tierney, Alexandra, Beauvais, Ariane, Kothary, Rashmi
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6856606/
https://www.ncbi.nlm.nih.gov/pubmed/31608604
http://dx.doi.org/10.1002/acn3.50920