The Effect of Various Doses of Phenylalanine Supplementation on Blood Phenylalanine and Tyrosine Concentrations in Tyrosinemia Type 1 Patients

Tyrosinemia type 1 (TT1) treatment with 2-(2-nitro-4-trifluormethyl-benzyl)-1,3-cyclohexanedione (NTBC) and a phenylalanine-tyrosine restricted diet is associated with low phenylalanine concentrations. Phenylalanine supplementation is prescribed without comprehensive consideration about its effect o...

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Detalles Bibliográficos
Autores principales: van Ginkel, Willem G., van Reemst, Hannah E., Kienstra, Nienke S., Daly, Anne, Rodenburg, Iris L., MacDonald, Anita, Burgerhof, Johannes G.M., de Blaauw, Pim, van de Krogt, Jennifer, Santra, Saikat, Heiner-Fokkema, M. Rebecca, van Spronsen, Francjan J.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2019
Materias:
Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6893509/
https://www.ncbi.nlm.nih.gov/pubmed/31752110
http://dx.doi.org/10.3390/nu11112816

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6893509/
https://www.ncbi.nlm.nih.gov/pubmed/31752110
http://dx.doi.org/10.3390/nu11112816

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