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Tracking muscle wasting and disease activity in facioscapulohumeral muscular dystrophy by qualitative longitudinal imaging

BACKGROUND: Facioscapulohumeral muscular dystrophy (FSHD) is one of the most frequent late‐onset muscular dystrophies, characterized by progressive fatty replacement and degeneration involving single muscles in an asynchronous manner. With clinical trials at the horizon in this disease, the knowledg...

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Detalles Bibliográficos
Autores principales: Monforte, Mauro, Laschena, Francesco, Ottaviani, Pierfrancesco, Bagnato, Maria Rosaria, Pichiecchio, Anna, Tasca, Giorgio, Ricci, Enzo
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6903444/
https://www.ncbi.nlm.nih.gov/pubmed/31668022
http://dx.doi.org/10.1002/jcsm.12473