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Sexual behaviour in a murine model of mucopolysaccharidosis type I (MPS I)

Mucopolysaccharidosis Type I (MPS I) is a rare genetic lysosomal storage disease caused by a mutation of IDUA gene. IDUA codes for α-L-iduronidase (IDUA), a lysosomal hydrolase that degrades glycosaminoglycans (GAGs): heparan sulphate and dermatan sulphate. GAGs are structural and signalling molecul...

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Detalles Bibliográficos
Autores principales: Barbosa Mendes, Ana, do Nascimento, Cinthia Castro, D’Almeida, Vânia
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Public Library of Science 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6910675/
https://www.ncbi.nlm.nih.gov/pubmed/31834922
http://dx.doi.org/10.1371/journal.pone.0220429