Myocardial Storage, Inflammation, and Cardiac Phenotype in Fabry Disease After One Year of Enzyme Replacement Therapy

Cardiac response to enzyme replacement therapy (ERT) in Fabry disease is typically assessed by measuring left ventricular mass index using echocardiography or cardiovascular magnetic resonance, but neither quantifies myocardial biology. Low native T1 in Fabry disease represents sphingolipid accumula...

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Detalles Bibliográficos
Autores principales: Nordin, Sabrina, Kozor, Rebecca, Vijapurapu, Ravi, Augusto, João B., Knott, Kristopher D., Captur, Gabriella, Treibel, Thomas A., Ramaswami, Uma, Tchan, Michel, Geberhiwot, Tarekegn, Steeds, Richard P., Hughes, Derralynn A., Moon, James C.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Lippincott Williams & Wilkins 2019
Materias:
Original Articles
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6924943/
https://www.ncbi.nlm.nih.gov/pubmed/31826677
http://dx.doi.org/10.1161/CIRCIMAGING.119.009430

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6924943/
https://www.ncbi.nlm.nih.gov/pubmed/31826677
http://dx.doi.org/10.1161/CIRCIMAGING.119.009430

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