Cargando…
Is fibrodysplasia ossificans progressiva an interleukin-1 driven auto-inflammatory syndrome?
BACKGROUND: Fibrodysplasia ossificans progressiva (FOP) is the most catastrophic form of heterotopic ossification, due to ongoing intracellular signaling through the bone morphogenic protein pathway. The paroxysmal appearance of inflammatory lumps and elevated inflammatory markers during flares, sug...
Autores principales: | Haviv, Ruby, Moshe, Veronica, De Benedetti, Fabrizio, Prencipe, Giusi, Rabinowicz, Noa, Uziel, Yosef |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2019
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6925442/ https://www.ncbi.nlm.nih.gov/pubmed/31864380 http://dx.doi.org/10.1186/s12969-019-0386-6 |
Ejemplares similares
-
Fibrodysplasia ossificans progressiva
por: Smit, Chané, et al.
Publicado: (2023) -
Recent Topics in Fibrodysplasia Ossificans Progressiva
por: Katagiri, Takenobu, et al.
Publicado: (2018) -
Fibrodysplasia Ossificans Progressiva: Clinical and Genetic Aspects
por: Pignolo, Robert J, et al.
Publicado: (2011) -
Quality of life of patients with fibrodysplasia ossificans progressiva
por: Ortiz-Agapito, Fernando, et al.
Publicado: (2015) -
Bone Resection Osteotomy in Fibrodysplasia Ossificans Progressiva
por: Colmenares-Bonilla, Douglas, et al.
Publicado: (2018)