Cargando…

Desquamative interstitial pneumonia in a non-smoker with neurofibromatosis type 1 (Von Recklinghausen syndrome)

Neurofibromatosis type 1 (NF1) is an autosomal dominant disorder with multiple systemic manifestations. Pulmonary involvement has been reported in the form of interstitial fibrosis, emphysema, pulmonary hypertension and thoracic neoplasm. We report a case of desquamative interstitial pneumonia in a...

Descripción completa

Detalles Bibliográficos
Autores principales: Ferrer, Gustavo, Saleh, Alwiya Omar, Tazelaar, Henry D, Arrossi, Andrea V
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BMJ Publishing Group 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6954786/
https://www.ncbi.nlm.nih.gov/pubmed/31924705
http://dx.doi.org/10.1136/bcr-2018-227379