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Early Left Ventricular Systolic Dysfunction Detected by Two-Dimensional Speckle-Tracking Echocardiography in Young Patients with Congenital Generalized Lipodystrophy

PURPOSE: Congenital generalized lipodystrophy (CGL) is a rare autosomal recessive disorder characterized by the absence of functional adipocytes resulting in ectopic lipid storage, metabolic disorders and early cardiovascular disease. Two-dimensional speckle-tracking (2D-STE) allows the detection of...

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Detalles Bibliográficos
Autores principales: Liberato, Christiane Bezerra Rocha, Olegario, Natália Bitar da Cunha, Fernandes, Virginia Oliveira, Montenegro, Ana Paula Dias Rangel, Lima, Grayce Ellen da Cruz Paiva, Batista, Lívia Aline de Araújo, Martins, Lívia Vasconcelos, Penaforte-Saboia, Jaquellyne Gurgel, Liberato, Ivan Lucas Rocha, Lopes, Larissa Ferreira, d’Alva, Catarina Brasil, Furtado, Frederico Luís Braz, Lima, Ricardo Luiz De Medeiros, Nóbrega, Lucia Helena Coelho, Lima, Josivan Gomes, Montenegro Junior, Renan Magalhães
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Dove 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6968814/
https://www.ncbi.nlm.nih.gov/pubmed/32021357
http://dx.doi.org/10.2147/DMSO.S233667