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Successful treatment of diffuse pulmonary lymphangiomatosis with sirolimus

Diffuse pulmonary lymphangiomatosis (DPL) is a rare disease characterized by uncontrolled proliferation of anastomosing lymphatic channels in the lungs, pleura and mediastinum. Several palliative treatment options have been suggested for this condition, such as surgical interventions, radiotherapy a...

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Detalles Bibliográficos
Autores principales: Gurskytė, Viktorija, Zeleckienė, Ingrida, Maskoliūnaitė, Vygantė, Mickys, Ugnius, Šileikienė, Virginija
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7013175/
https://www.ncbi.nlm.nih.gov/pubmed/32071853
http://dx.doi.org/10.1016/j.rmcr.2020.101014