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Small Molecule Anion Carriers Correct Abnormal Airway Surface Liquid Properties in Cystic Fibrosis Airway Epithelia

Cystic fibrosis (CF) is a genetic disease characterized by the lack of cystic fibrosis transmembrane conductance regulator (CFTR) protein expressed in epithelial cells. The resulting defective chloride and bicarbonate secretion and imbalance of the transepithelial homeostasis lead to abnormal airway...

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Detalles Bibliográficos
Autores principales: Gianotti, Ambra, Capurro, Valeria, Delpiano, Livia, Mielczarek, Marcin, García-Valverde, María, Carreira-Barral, Israel, Ludovico, Alessandra, Fiore, Michele, Baroni, Debora, Moran, Oscar, Quesada, Roberto, Caci, Emanuela
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7073096/
https://www.ncbi.nlm.nih.gov/pubmed/32098269
http://dx.doi.org/10.3390/ijms21041488