Cargando…

Hexacosenoyl-CoA is the most abundant very long-chain acyl-CoA in ATP binding cassette transporter D1-deficient cells

X-linked adrenoleukodystrophy (X-ALD) is an inherited disorder caused by deleterious mutations in the ABCD1 gene. The ABCD1 protein transports very long-chain FAs (VLCFAs) from the cytosol into the peroxisome where the VLCFAs are degraded through β-oxidation. ABCD1 dysfunction leads to VLCFA accumul...

Descripción completa

Detalles Bibliográficos
Autores principales:	Hama, Kotaro, Fujiwara, Yuko, Takashima, Shigeo, Hayashi, Yasuhiro, Yamashita, Atsushi, Shimozawa, Nobuyuki, Yokoyama, Kazuaki
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	The American Society for Biochemistry and Molecular Biology 2020
Materias:	Patient-Oriented and Epidemiological Research
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7112142/ https://www.ncbi.nlm.nih.gov/pubmed/32075856 http://dx.doi.org/10.1194/jlr.P119000325

Ejemplares similares

Acetyl-CoA carboxylase inhibitor increases LDL-apoB production rate in NASH with cirrhosis: prevention by fenofibrate
por: Dandan, Mohamad, et al.
Publicado: (2023)

RICE ACYL-COA-BINDING PROTEIN6 Affects Acyl-CoA Homeostasis and Growth in Rice
por: Meng, Wei, et al.
Publicado: (2020)

Fatty acyl-CoA reductases of birds
por: Hellenbrand, Janine, et al.
Publicado: (2011)

Acyl-CoA-dependent and acyl-CoA-independent avocado acyltransferases positively influence oleic acid content in nonseed triacylglycerols
por: Behera, Jyoti, et al.
Publicado: (2023)

Translocation of acyl-CoA oxidase into peroxisomes requires ATP hydrolysis but not a membrane potential
Publicado: (1987)

Fatty Acyl-CoA Reductase 1 Deficiency
por: Swisher, Charles N.
Publicado: (2015)

The Physiological and Pathological Role of Acyl-CoA Oxidation
por: Szrok-Jurga, Sylwia, et al.
Publicado: (2023)

A Liver-Specific Defect of Acyl-CoA Degradation Produces Hyperammonemia, Hypoglycemia and a Distinct Hepatic Acyl-CoA Pattern
por: Gauthier, Nicolas, et al.
Publicado: (2013)

Erratum: Acyl-CoA-dependent and acyl-CoA-independent avocado acyltransferases positively influence oleic acid content in nonseed triacylglycerols
Publicado: (2023)

Structural basis for substrate specificity of methylsuccinyl-CoA dehydrogenase, an unusual member of the acyl-CoA dehydrogenase family
por: Schwander, Thomas, et al.
Publicado: (2018)

CR reprograms acetyl‐CoA metabolism and induces long‐chain acyl‐CoA dehydrogenase and CrAT expression
por: Mezhnina, Volha, et al.
Publicado: (2020)

A Single LC-MS/MS Analysis to Quantify CoA Biosynthetic Intermediates and Short-Chain Acyl CoAs
por: Jones, Anthony E., et al.
Publicado: (2021)

Combined isobutyryl‐CoA and multiple acyl‐CoA dehydrogenase deficiency in a boy with altered riboflavin homeostasis
por: Tummolo, Albina, et al.
Publicado: (2022)

Cardiac Hypertrophy in Mice with Long-Chain Acyl-CoA Dehydrogenase (LCAD) or Very Long-Chain Acyl-CoA Dehydrogenase (VLCAD) Deficiency
por: Cox, Keith B., et al.
Publicado: (2009)

Acyl-CoA thioesterase activity of peroxisomal ABC protein ABCD1 is required for the transport of very long-chain acyl-CoA into peroxisomes
por: Kawaguchi, Kosuke, et al.
Publicado: (2021)

A chemical catalyst enabling histone acylation with endogenous acyl-CoA
por: Habazaki, Misuzu, et al.
Publicado: (2023)

Metabolic and Tissue-Specific Regulation of Acyl-CoA Metabolism
por: Ellis, Jessica M., et al.
Publicado: (2015)

Compartmentalised acyl-CoA metabolism and roles in chromatin regulation
por: Trefely, Sophie, et al.
Publicado: (2020)

In vitro and in vivo downregulation of the ATP binding cassette transporter B1 by the HMG-CoA reductase inhibitor simvastatin
por: Atil, Bihter, et al.
Publicado: (2015)

Glycosphingolipids with Very Long-Chain Fatty Acids Accumulate in Fibroblasts from Adrenoleukodystrophy Patients
por: Fujiwara, Yuko, et al.
Publicado: (2021)

Clinical aspects of short-chain acyl-CoA dehydrogenase deficiency
por: van Maldegem, Bianca T., et al.
Publicado: (2010)

Giardia fatty acyl-CoA synthetases as potential drug targets
por: Guo, Fengguang, et al.
Publicado: (2015)

Intracellular Long-Chain Acyl CoAs Activate TRPV1 Channels
por: Yu, Yi, et al.
Publicado: (2014)

Targeting Long Chain Acyl-CoA Synthetases for Cancer Therapy
por: Rossi Sebastiano, Matteo, et al.
Publicado: (2019)

Effects of short‐chain acyl‐CoA dehydrogenase on cardiomyocyte apoptosis
por: Zeng, Zhenhua, et al.
Publicado: (2016)

Functional characterization of acyl-CoA binding protein in Neospora caninum
por: Zhou, Bingxin, et al.
Publicado: (2020)

Pancreatitis in multiple acyl CoA dehydrogenase deficiency: An underdiagnosed complication
por: Elkhateeb, Nour, et al.
Publicado: (2020)

In silico Analysis of Acyl-CoA-Binding Protein Expression in Soybean
por: Azlan, Nur Syifaq, et al.
Publicado: (2021)

Characterization of trans-3-Methylglutaconyl CoA-Dependent Protein Acylation
por: Jennings, Elizabeth A., et al.
Publicado: (2023)

A novel multidomain acyl-CoA carboxylase in Saccharopolyspora erythraea provides malonyl-CoA for de novo fatty acid biosynthesis
por: Livieri, Andrea L., et al.
Publicado: (2019)

Specific regulation of low-abundance transcript variants encoding human Acyl-CoA binding protein (ACBP) isoforms
por: Nitz, Inke, et al.
Publicado: (2011)

MadR mediates acyl CoA-dependent regulation of mycolic acid desaturation in mycobacteria
por: Cooper, Charlotte, et al.
Publicado: (2022)

Medium-Chain Acyl-CoA Dehydrogenase Deficiency in Gene-Targeted Mice
por: Tolwani, Ravi J, et al.
Publicado: (2005)

Diversity and dispersal of a ubiquitous protein family: acyl-CoA dehydrogenases
por: Shen, Yao-Qing, et al.
Publicado: (2009)

Medium-Chain Acyl-CoA Dehydrogenase Deficiency in an Infant with Dilated Cardiomyopathy
por: Marcì, Marcello, et al.
Publicado: (2009)

The Inflammatory Response in Acyl-CoA Oxidase 1 Deficiency (Pseudoneonatal Adrenoleukodystrophy)
por: El Hajj, H. I., et al.
Publicado: (2012)

Correction: Intracellular Long-Chain Acyl CoAs Activate TRPV1 Channels
Publicado: (2015)

Computational Prediction of acyl-coA Binding Proteins Structure in Brassica napus
por: Raboanatahiry, Nadia Haingotiana, et al.
Publicado: (2015)

Medium chain acyl-CoA dehydrogenase deficiency in a premature infant
por: Dobrowolski, Steven F., et al.
Publicado: (2017)

Functional and Structural Diversity of Acyl-coA Binding Proteins in Oil Crops
por: Raboanatahiry, Nadia, et al.
Publicado: (2018)

Cannot write session to /tmp/vufind_sessions/sess_df1qdtv2721ctfvved12j78g9s